IRJS Navigation
About
Publication Ethics
Call For Paper
Guide to Authors
Editorial Board
Submit Manuscript
Articles
Viewing Options
[View Abstract]
[View Full Text PDF]
[View Full Text PDF]
Authors Articles on Google Scholar
Noomen Haoues
Haithem Zaafouri*
Manel Mabrouk
Rabii Noomene
Mariam Bel Hadj Salah
Abderraouf Cherif
Ahmed Bouhafa
Anis Ben Maamer
Skander Mrad
Authors Articles on Pubmed
Noomen Haoues
Haithem Zaafouri*
Manel Mabrouk
Rabii Noomene
Mariam Bel Hadj Salah
Abderraouf Cherif
Ahmed Bouhafa
Anis Ben Maamer
Skander Mrad
Preferences
Email this Article to a friend
Print this Article
Statistics
Viewed: 1,400
Forwarded: 0
Printed: 152
Downloaded: 2,496
Browse Journals By Category
Agriculture and Food Sciences
Biological Sciences
Education and Arts
Engineering
Environmental Sciences
Medical Sciences
Pharmaceutical Sciences
Physical and Natural Sciences
Social Sciences

Newsletters Subscription

International Research Journal of Surgery

Hirschsprung’s disease in adults: Clinical and therapeutic features

Haithem Zaafouri*, Skander Mrad, Manel Mabrouk, Noomen Haoues, Mariam Bel Hadj Salah, Rabii Noomene, Ahmed Bouhafa, Anis Ben Maamer, Abderraouf Cherif

Accepted 19 February, 2015.

Citation: Zaafouri H, Mrad S, Mabrouk M, Haoues N, Salah MBH, Noomene R, Ahmed Bouhafa, Anis Ben Maamer and Abderraouf Cherif (2015). Hirschsprung’s disease in adults: Clinical and therapeutic features. International Research Journal of Surgery, 2(1): 009-017.

Copyright: © 2015 Zaafouri et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are cited.

Abstract

Hirschsprung’s disease (HD) is rare in adults and it is thus often undiagnosed or misdiagnosed. Through this series of 12 patients we try to study the clinical characteristics of this pathology, to define its diagnostic clues and to assess the different therapeutic approaches.

Definitive diagnosis is established on histology of specimens from the rectum and colon. The disease involved the rectum and the sigmoid colon in 2 patients and was confined to the rectum, in the 10 others.

Treatment was in all cases surgical consisting of recto-colic resection associated with coloanal anastomosis and a protective right lateral ileostomy.

We conclude that Hirschsprung’s disease is rare in adults but by no means exceptional. It should be considered in young adults with a history of chronic constipation. Diagnosis is first of all clinical. When barium enema appearances are pathognomonic we needn’t resort to histology to confirm the diagnosis. Anorectal manometry does not usually show RAIR. Current primary treatment of HD diagnosed in adults consists mainly of surgical resection.

Key words: Hirschsprung, rectoanal inhibitory reflex, intestinal obstruction, coloanal anastomosis, Duhamel.

Related Articles